• Source: Carnitine O-palmitoyltransferase

Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.




Molecules















Pathway






Human forms


There are four different forms of CPT in humans:

CPT1A – associated with Carnitine palmitoyltransferase I deficiency
CPT1B
CPT1C
CPT2 – associated with carnitine palmitoyltransferase II deficiency




See also


Fatty acid degradation § Transport into the mitochondrial matrix




References






External links


PDOC00402 – Acyltransferases ChoActase / COT / CPT family in PROSITE
Choline/Carnitine o-acyltransferase family in Pfam
UMich Orientation of Proteins in Membranes protein/pdbid-2h4t
Carnitine+O-Palmitoyltransferase at the U.S. National Library of Medicine Medical Subject Headings (MeSH)

Kata Kunci Pencarian:

• Carnitine O-palmitoyltransferase
• Carnitine palmitoyltransferase I
• Carnitine palmitoyltransferase II deficiency
• Carnitine palmitoyltransferase II
• Carnitine
• Integral monotopic protein
• Palmitoylcarnitine
• Carnitine O-acetyltransferase
• Carnitine O-octanoyltransferase
• Inner mitochondrial membrane