• Source: Familial Alzheimer-like prion disease

Familial Alzheimer-like prion disease is an exceptionally rare inherited prion disease. Its name comes from its presentation, which is similar to Alzheimer's disease.




Symptoms


This disease is unusual in that, unlike other prion diseases, it does not present with myoclonus or ataxia. Instead, the initial presentation involves anxiety, depression, and memory impairment before progression into dementia. This dementia has a slow course, also atypical for a prion disease, and will eventually lead to the death of the patient years after onset.




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GARD

Kata Kunci Pencarian:

• Familial Alzheimer-like prion disease
• Prion
• Transmissible spongiform encephalopathy
• Fatal insomnia
• Creutzfeldt–Jakob disease
• Camel spongiform encephalopathy
• ALS
• Proteinopathy
• Parkinson's disease
• Amyloid