• Source: Familial osteodysplasia, Anderson type
  • Familial osteodysplasia, Anderson type is a rare genetic disorder which is characterized by cranio-facial dysmorphisms and multiple skeletal anomalies. Hyperuricemia, hypertension and high erythrocyte sedimentation rates have also been reported. Approximately 6 cases have been reported in medical literature. This disorder is thought to be inherited in an autosomal recessive manner.


    Description


    People with this disorder often show the following symptoms:


    = Craniofacial

    =
    Underdevelopment of midface
    Flat, broad nasal bridge
    Thin, prognathic mandible
    Pointy chin
    Malocclusion
    Underdeveloped teeth


    = Skeletal

    =
    Scoliosis
    Thinning of the calvaria
    Pointy spinous processes
    Clinodactyly
    Phalangeal dysplasia
    Additional symptoms include hyperuricemia, high erythrocyte sedimentation rates and hypertension.


    Etimology


    This condition was first discovered in 1972 by L G Anderson et al. and J S Buchignani et al. described the case of 5 siblings and their dad, 4 out of the 5 siblings had recurrent mandibular fractures and cranio-facial dysmorphisms, such as prominent earlobes. These 4 siblings also had hyperuricemia and 3 out of those 4 siblings had hypertension. Their father had hyperuricemia and hypertension but was otherwise unaffected. The siblings were the result of consanguineous Irish parents.


    References

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